International Journal of Infertility & Fetal Medicine

Register      Login

VOLUME 8 , ISSUE 1 ( January-April, 2017 ) > List of Articles

CASE REPORT

Parietal Cranium Bifidum: A Rare Presentation

Sivakami Rathinam, Rameshkumar Rudrappa, Bhavishya Talluri

Citation Information : Rathinam S, Rudrappa R, Talluri B. Parietal Cranium Bifidum: A Rare Presentation. Int J Infertil Fetal Med 2017; 8 (1):41-44.

DOI: 10.5005/jp-journals-10016-1146

License: CC BY-NC 4.0

Published Online: 01-04-2017

Copyright Statement:  Copyright © 2017; The Author(s).


Abstract

Aim

To enlighten the readers regarding rare and distinct presentation of fetal encephalocele in parietal location and its significance.

Background

Cranium bifidum is a defect in the cranium through which there can be herniation of intracranial contents. If the content of herniation is meninges, it is called meningocele and if it contains brain tissue in addition to meninges, it is called meningoencephalocele or encephalocele. The incidence of encephalocele is 1 in 4,000 live births. The most common location is the occipital region (75%) followed by frontoethmoidal (15%), which is common in Asian population, and rarest is the basal followed by parietal locations. The exact incidence of parietal encephalocele is not available due to its rarity.

Case report

We present a case of a 24-year-old primigravida female in second trimester who came for antenatal scan to rule out anomalies. On examination by ultrasonography, we found a large cerebriform soft tissue herniating through a defect in skull vault from the vertex region with secondary microcephaly

Conclusion

Here we give an overview of rarest form of encephalocele in parietal region, which grossly differs from the already reported parietal encephaloceles of atretic type presenting as small skin-covered subscalp lesions that contain Meninges and neural and glial rests. In our case, the encephalocele was distinct, being larger in size with normal brain parenchyma as the major content of the herniating sac.

Clinical significance

Only few cases of parietal encephalocele is reported in the literature, that too of atretic type. Apart from being the rarest form, this variant is found to be associated with poor prognosis.

How to cite this article

Rathinam S, Rudrappa R, Talluri B. Parietal Cranium Bifidum: A Rare Presentation. Int J Infertil Fetal Med 2017;8(1):41-44.


PDF Share
  1. Lumps and bumps on the head in children: use of CT and MR imaging in solving the clinical diagnostic dilemma. Radiographics 2004 Nov;24(6):1655-1674.
  2. Atretic parietal encephalocele – an unusual diagnosis. Med J Armed Forces India 2013 Jan;69(1):83-85.
  3. Atretic parietal cephalocoeles revisited: an enlarging clinical and imaging spectrum? AJNR Am J Neuroradiol 1998 Apr;19(4):791-795.
  4. Atretic meningocele: etiopathogenesis, frequency, anomaly associations and imaging findings. Austin J Radiol 2015;2(1): 1011.
  5. Magnetic resonance imaging of the fetal brain and spine: an increasingly important tool in prenatal diagnosis: part 2. AJNR Am J Neuroradiol 2006 Oct;27(9):1807-1814.
PDF Share
PDF Share

© Jaypee Brothers Medical Publishers (P) LTD.